ACOX1 Rabbit Polyclonal Antibody
Catalog# ER1919-52
ACOX1 Rabbit Polyclonal Antibody
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WB
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Human
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Mouse
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Rat
概述
产品名称
ACOX1 Rabbit Polyclonal Antibody
抗体类型
Rabbit Polyclonal Antibody
免疫原
KLH conjugated synthetic peptide derived from human ACOX1: 221-320/660
种属反应性
Human, Mouse, Rat
验证应用
WB
分子量
74 kDa
偶联
unconjugated
产品特性
形态
Liquid
存放说明
Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.
存储缓冲液
0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
亚型
IgG
纯化方式
Protein A affinity purified.
应用稀释度
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WB
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1:500-2000
靶点
功能
Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.
背景文献
暂无
亚细胞定位
Peroxisome.
别名
ACOX antibody
ACOX1 antibody
ACOX1_HUMAN antibody
Acyl CoA oxidase 1 palmitoyl antibody
Acyl CoA oxidase straight chain antibody
AOX antibody
EC 1.3.3.6 antibody
PALMCOX antibody
Palmitoyl CoA oxidase antibody
Palmitoyl-CoA oxidase antibody
展开图片
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Sample:
Lane 1: Mouse Cerebrum tissue lysates
Lane 2: Mouse Heart tissue lysates
Lane 3: Rat Cerebrum tissue lysates
Lane 4: Human HepG2 cell lysates
Lane 5: Human MCF-7 cell lysates
Primary: Anti-ACOX1 (ER1919-52) at 1/1000 dilution
Secondary: IRDye800CW Goat Anti-Rabbit IgG at 1/20000 dilution
Predicted band size: 74 kDa
Observed band size: 73 kDa
请注意: All products are "FOR RESEARCH USE ONLY AND ARE NOT INTENDED FOR DIAGNOSTIC OR THERAPEUTIC USE"